Thrombotic thrombocytopenic purpura

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In medicine and hematology, thrombotic thrombocytopenic purpura (TTP) is "an acquired, congenital, or familial disorder caused by platelet aggregation with thrombosis in terminal arterioles and capillaries. Clinical features include thrombocytopenia; hemolytic anemia; azotemia; fever; and thrombotic microangiopathy. The classical form also includes neurological symptoms and end-organ damage, such as renal failure."[1]

Patients with primary TTP may have low von Willebrand factor-degrading protease (ADAMTS13 protein) which allows thrombi due to von Willebrand factor (vWF).[2]

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